Abstract：Objective To summarize the surgical treatment of congenital heart diseases (CHD) with diminutive pulmonary vessels.Methods From Jan. 2000 to Dec. 2013, the clinical data of 252 children of CHD with diminutive pulmonary vessels in our department were analyzed retrospectively. After the diagnosis was confirmed by performing cardiac echocardiography, magnetic resonance imaging or spiral CT and other tests, an appropriate surgery was selected according to the development of left and right ventricular and pulmonary arteries. Anatomical correction surgery was performed in 215 cases, and physical or palliative surgery was performed in other 37 cases. All cases were given full sedation, proper posture, circulation and respiratory support after the operation.Results The cardiopulmonary bypass time was (116.41±26.34) min, the aortic cross-clamping time was (72.65±25.41) min, the postoperative ventilation time was (18.42±11.83) min, the average amount of application dopamine was (8.02±2.14) mg·kg-1·min-1, intensive care time was (71.5±25.4) h, postoperative hospital stay time was (9.7±5.4)days. Operative death and surgical complications occurred in 13 and 54 cases respectively. The follow-up time was from six months to ten years. The artificial material of a patient was obstructed completely one year later after B-T shunting procedure. Calculation nearby right ventricular outflow tract occurred in 4 cases without unusual function. One case underwent total cava pulmonany correction operation suffered from pulmonary vessels fistula 4 years later. There was no death in middle and long term follow-up.Conclusions The Objective and comprehensive assessment of preoperative imaging, the correct choice of operation and postoperative care and treatment can greatly improve the surgery, reduce the incidence of surgical complications and mortality.
施超,刘学刚,唐震,王祖义,李小军,刘戈,张雷. 肺血管发育不良复杂先天性心脏病252例的外科治疗[J]. 中华解剖与临床杂志, 2014, 19(3): 187-190.
Shi Chao, Liu Xuegang, Tang Zhen, Wang Zhuyi, Li Xiaojun, Liu Ge, Zhang Lei. Surgical treatment for congenital heart diseases with diminutive pulmonary vessels. Chinese Journal of Anatomy and Clinics, 2014, 19(3): 187-190.
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