Abstract:Objective To summarize the experience in the anatomical diagnosis and surgical treatment of double chambered right ventricule.Methods From September 2001 to June 2014, 76 patients were admitted in our department. The resection was made through atrialtomy-right ventricular outflow tract incision in 58 patients (group A), through atrialtomy in 11 patients or through atrialtomy-pulmonary arteriotomy in 7 patients (group B) .Results The 76 cases of patients were successfully completed the operation. There were no any difficulties in the termination of cardiopulmonary bypass, no bleeding and other operation condition. The cardiopulmonary bypass time, postoperative average dosage of dopamine in 24 hours, ventilation time, postoperative drainage volume in 24 hours and the incidence of right bundle branch block in group A were higher than those in group B, the differences were statistically significant (all P values<0.01). However, the dredging postoperative systolic pressure difference and aortic cross clamping time in group A had no statistically significant differences compared with those ingroup B (all P values>0.05). There were no deaths. Postoperative complications included 5 cases of low cardiac output syndrome, 6 cases of severe arrhythmia, 1 case of respiratory failure. They were all cured after timely and correct treatment. Follow up was extended 5 months to 13 years in the recovered patients. There were no any correlated complications.Conclusions It is critical and essential for a successful operation to perfectly comprehend double chambered right ventricule pathoanatomy, correctly identify anomalous muscle bundle and effecttively deoppilate right ventricular outflow tract. Both trans right ventricular outflow tract stenosis and transatrial approach can relief right ventricular outflow tract stenosis obstruction, but the latter seems have better early and mid-term effects.
葛圣林,车轰,周汝元,何维来,张士兵,李峰,张成鑫,冯俊波,郭志祥. 右室双腔心的外科治疗[J]. 中华解剖与临床杂志, 2014, 19(3): 191-194.
Ge Shenglin, Che Hong, Zhou Ruyuan, He Weilai, Zhang Shibing, Li Feng, Zhang Chengxin, Feng Junbo, Guo Zhixiang. Surgical treatment of double chambered right ventricule. Chinese Journal of Anatomy and Clinics, 2014, 19(3): 191-194.
Mohsen A, Rahman F, Ikram S. Anomalous muscle bundles causing double-chambered right ventricle in adults[J]. J Invasive Cardiol, 2013 , 25(12): E212-E213.
[3]
Kouache M, Babakhoya A, Labib S, et al. Repair of isolated double-chambered right ventricle[J]. Afr J Paediatr Surg, 2013, 10(2): 199-200.
[4]
Animasahun BA, Ekure EN, Njokanma OF. Double-chambered right ventricle: an uncommon congenital heart disease. Case report and literature review[J]. Cardiovasc J Afr, 2011 , 22 (5): 274-277.
[5]
Oliver JM, Garrido A, González A, et al. Rapid progression of midventricular obstruction in adults with double-chambered right ventricle[J]. J Thorac Cardiovasc Surg, 2003, 126(3): 711-717.
[6]
Darwazah AK, Eida M, Bader V, et al. Surgical management of double-chambered right ventricle in adults[J]. Tex Heart Inst J, 2011, 38(3): 301-304.
[7]
Kottayil BP, Dharan BS, Pillai VV, et al. Surgical repair of double-chambered right ventricle in adulthood[J]. Asian Cardiovasc Thorac Ann, 2011, 19(1): 57-60.
[8]
Telagh R, Alexi-Meskishvili V, Hetzer R, et al. Initial clinical manifestations and mid-and long-term results after surgical repair of double-chambered right ventricle in children and adults[J]. Cardiol Young, 2008, 18(3): 268-74.
[9]
Loukas M, Housman B, Blaak C, et al. Double-chambered right ventricle: a review[J]. Cardiovasc Pathol, 2013, 22(6): 417-23.
[10]
Selvaraj RJ, Gobu P, Ashida TS, et al. Ventricular tachycardia in repaired double chambered right ventricle-identification of the substrate and successful ablation[J]. Indian Pacing Electrophysiol J, 2012, 12(1): 27-31.